Morbihan disease complicated by dermatosis neglecta: An unique presentation.
Identifieur interne : 000360 ( Main/Exploration ); précédent : 000359; suivant : 000361Morbihan disease complicated by dermatosis neglecta: An unique presentation.
Auteurs : Ariel E. Eber [États-Unis] ; Stephanie Mlacker [États-Unis] ; Sebastian Verne [États-Unis] ; Robert Griffith [États-Unis] ; Jennifer Ledon [États-Unis] ; Marina Perper [États-Unis] ; Keyvan Nouri [États-Unis] ; Jeong Hee Cho-Vega [États-Unis]Source :
- Journal of cutaneous pathology [ 1600-0560 ] ; 2017.
Descripteurs français
- KwdFr :
- MESH :
- anatomopathologie : Dermatoses faciales, Oedème, Rosacée, Érythème.
- Adulte d'âge moyen, Dermatoses faciales, Femelle, Humains, Oedème, Rosacée, Érythème.
English descriptors
- KwdEn :
- MESH :
- complications : Edema, Erythema, Facial Dermatoses, Rosacea.
- pathology : Edema, Erythema, Facial Dermatoses, Rosacea.
- Female, Humans, Middle Aged.
Abstract
Morbihan disease, also referred to as solid facial edema, or rosacea lymphedema, is a rare disorder that involves chronic erythema and solid edema of the cheeks, eyelids, forehead and glabella and may arise as a complication of acne vulgaris or rosacea. Of note, it may be the only initial presenting symptom of these associated diseases. Few cases have been described in the literature, as its first description by Robert Degos in 1957. The condition is characterized by its chronicity, a typical clinical appearance and the lack of specific histopathologic or laboratory findings. The condition may wax and wane but typically does not resolve without treatment. Many cases of this condition tend to be recalcitrant to therapy, with topical and oral antibiotics regimens commonly used for rosacea generally being ineffective. The disease may easily go undiagnosed, as it mimics other more common skin conditions. We present a case of originally undiagnosed Morbihan disease mistaken for an atypical allergic rash, resistant to treatment, and complicated by dermatosis neglecta.
DOI: 10.1111/cup.12902
PubMed: 28097676
Affiliations:
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xml:lang="en"><term>Edema</term><term>Erythema</term><term>Facial Dermatoses</term><term>Rosacea</term></keywords><keywords scheme="MESH" xml:lang="en"><term>Female</term><term>Humans</term><term>Middle Aged</term></keywords><keywords scheme="MESH" xml:lang="fr"><term>Adulte d'âge moyen</term><term>Dermatoses faciales</term><term>Femelle</term><term>Humains</term><term>Oedème</term><term>Rosacée</term><term>Érythème</term></keywords></textClass></profileDesc></teiHeader><front><div type="abstract" xml:lang="en">Morbihan disease, also referred to as solid facial edema, or rosacea lymphedema, is a rare disorder that involves chronic erythema and solid edema of the cheeks, eyelids, forehead and glabella and may arise as a complication of acne vulgaris or rosacea. Of note, it may be the only initial presenting symptom of these associated diseases. Few cases have been described in the literature, as its first description by Robert Degos in 1957. The condition is characterized by its chronicity, a typical clinical appearance and the lack of specific histopathologic or laboratory findings. The condition may wax and wane but typically does not resolve without treatment. Many cases of this condition tend to be recalcitrant to therapy, with topical and oral antibiotics regimens commonly used for rosacea generally being ineffective. The disease may easily go undiagnosed, as it mimics other more common skin conditions. We present a case of originally undiagnosed Morbihan disease mistaken for an atypical allergic rash, resistant to treatment, and complicated by dermatosis neglecta.</div></front></TEI><affiliations><list><country><li>États-Unis</li></country><region><li>Floride</li></region></list><tree><country name="États-Unis"><region name="Floride"><name sortKey="Eber, Ariel E" sort="Eber, Ariel E" uniqKey="Eber A" first="Ariel E" last="Eber">Ariel E. Eber</name></region><name sortKey="Cho Vega, Jeong Hee" sort="Cho Vega, Jeong Hee" uniqKey="Cho Vega J" first="Jeong Hee" last="Cho-Vega">Jeong Hee Cho-Vega</name><name sortKey="Griffith, Robert" sort="Griffith, Robert" uniqKey="Griffith R" first="Robert" last="Griffith">Robert Griffith</name><name sortKey="Ledon, Jennifer" sort="Ledon, Jennifer" uniqKey="Ledon J" first="Jennifer" last="Ledon">Jennifer Ledon</name><name sortKey="Mlacker, Stephanie" sort="Mlacker, Stephanie" uniqKey="Mlacker S" first="Stephanie" last="Mlacker">Stephanie Mlacker</name><name sortKey="Nouri, Keyvan" sort="Nouri, Keyvan" uniqKey="Nouri K" first="Keyvan" last="Nouri">Keyvan Nouri</name><name sortKey="Perper, Marina" sort="Perper, Marina" uniqKey="Perper M" first="Marina" last="Perper">Marina Perper</name><name sortKey="Verne, Sebastian" sort="Verne, Sebastian" uniqKey="Verne S" first="Sebastian" last="Verne">Sebastian Verne</name></country></tree></affiliations></record>Pour manipuler ce document sous Unix (Dilib)
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